Congenital anomalies encompass structural or functional defects that occur during intrauterine life and are identified at birth, during infancy, or later in life. In pediatric surgery, these anomalies often require surgical reconstruction. Key conditions managed include anorectal malformations (imperforate anus), biliary atresia, choledochal cysts, Hirschsprung disease, and neural tube defects. Early detection through prenatal ultrasound screening allows for timely surgical planning and improves neonatal survival outcomes.